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Description
Category: Carbohydrates and Derivatives, Fluorescent Labels and Indicators /// Appearance: White Solid /// Application Notes: A fluorogenic substrate used for the diagnosis of GM2 gangliosidoses in leukocytes. Genetic defects in human b-hexosaminidase isozymes (Hex A and Hex B) result in various clinical and biochemical types of GM2 gangliosidosis. They include Tay Sachs disease, Sandhoff disease and other forms. /// References: Clinical Genetics, 26, 318 (1984)| Bayleran, J., et al.: Clin. Chem. Acta 143, 73 (1984)
Structure formula

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